Loading...
Dernières publications
-
Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
-
Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
-
Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
60 %
Mots clés
Adipose tissue
BINDING SPECIFICITY
Metabolism
Oculopharyngeal muscular dystrophy
Regeneration
FSHD
Myositis
AUTOPHAGY
Dysferlinopathy
Dystrophin
Lamins
AAV vectors
Autoimmune diseases
Geriatric assessment
Duchenne muscular dystrophy
2-D PAGE
ALS
Alphavirus
Differentiation
Bioinformatics
Muscle dystrophy
Thérapie génique
Cross-bridge kinetics
Intercellular communication
Annexin A2
RNA
Triplet expansion disease
Autologous
PABPN1
Calcium
Anti-fibrotic pharmacotherapies
Muscle fibrosis
Muscle stem cells
Bioinformatique
Myotube
DMD
Myoblasts
Satellite cells
Pharyngeal muscle
Aggregate
OPMD
Exon-skipping
Nuclear envelope
Atrophy
Andermann syndrome
Gene therapy
Dystrophie musculaire oculopharyngée
Aged
CD49d
APOPTOSIS
Human
Muscle strength
Skeletal muscle
FAPs
CS
Ageing
GENE
C2 domains
Biomarker
Xenograft
Fibrosis
Myopathies
Myopathy
ARN
MUTATIONS
Antisens oligonucleotides
Anti-acetylcholine receptor antibodies
Accelerometry
Muscle
Agrégats de PABPN1
Cell therapy
Arbovirus
Transcriptomics
Satellite cell
AAV
Pax7
C2C12 cells
Myoblast
Antiserum
Myogenesis
Haploinsufficiency
Actin
Biopsies humaines
Gene replacement
Neuromuscular junction NMJ
Myosin
DNA methylation
PABPN1 agregates
AChR antibodies
Aav-U7
Akt
Sarcopenia
CNOT6L
Functional genomics
Botulinum neurotoxin
Inflammation
Bile salt hydrolases
Alzheimer's disease
DUX4
Dysferlin